Clinical Presentation, Natural History, and Therapeutic Approach in Patients with Solitary Fibrous Tumor: A Retrospective Analysis.
Patrick SchöffskiI TimmermansD HompesM StasF SinnaeveP De LeynW CoosemansD Van RaemdonckE HaubenRaf M E SciotP ClementO BechterB BeuselinckF J S H Woei-A-JinH DumezP NafteuxT WesselsPublished in: Sarcoma (2020)
SFT is an orphan malignancy with a highly variable clinical course and a considerable risk of local failure and metachronous metastasis. Surgery is the only curative option; palliative systemic therapy is used in inoperable/metastatic cases but achieves low response rates. The highest response rates are seen with pazopanib in second/third line.