Nationwide retrospective observational study of idiopathic dendriform pulmonary ossification: clinical features with a progressive phenotype.
Yasuhiko NishiokaYuko ToyodaRyoko EgashiraTakeshi JohkohYasuhiro TerasakiAkira HebisawaKinya AbeTomohisa BabaYuji FujikuraEtsuo FujitaNaoki HamadaTomohiro HandaYoshinori HasegawaKoko HidakaTakeshi HisadaShu HisataChisato HonjoKazuya IchikadoYoshikazu InoueShinyu IzumiMotoyasu KatoTakumi KishimotoMasaki OkamotoKeisuke MikiMasamichi MineshitaYutaro NakamuraSusumu SakamotoMasaaki SanoYoshikazu TsukadaMari YamasueYoshimi BandoSakae HommaKoichi HagiwaraTakafumi SudaNaohiko InasePublished in: BMJ open respiratory research (2022)
IDPO develops at a young age with gradually progressive phenotype. Further research and long-term (>20 years) follow-up are required to clarify the pathogenesis and clinical findings in IDPO.