The Klinefelter Syndrome and Testicular Sperm Retrieval Outcomes.
Rosália SáLuís FerrazAlberto BarrosMário SousaPublished in: Genes (2023)
Klinefelter syndrome (KS), caused by the presence of an extra X chromosome, is the most prevalent chromosomal sexual anomaly, with an estimated incidence of 1:500/1000 per male live birth (karyotype 47,XXY). High stature, tiny testicles, small penis, gynecomastia, feminine body proportions and hair, visceral obesity, and testicular failure are all symptoms of KS. Endocrine (osteoporosis, obesity, diabetes), musculoskeletal, cardiovascular, autoimmune disorders, cancer, neurocognitive disabilities, and infertility are also outcomes of KS. Causal theories are discussed in addition to hormonal characteristics and testicular histology. The retrieval of spermatozoa from the testicles for subsequent use in assisted reproduction treatments is discussed in the final sections. Despite testicular atrophy, reproductive treatments allow excellent results, with rates of 40-60% of spermatozoa recovery, 60% of clinical pregnancy, and 50% of newborns. This is followed by a review on the predictive factors for successful sperm retrieval. The risks of passing on the genetic defect to children are also discussed. Although the risk is low (0.63%) when compared to the general population (0.5-1%), patients should be informed about embryo selection through pre-implantation genetic testing (avoids clinical termination of pregnancy). Finally, readers are directed to a number of reviews where they can enhance their understanding of comprehensive diagnosis, clinical care, and fertility preservation.
Keyphrases
- type diabetes
- germ cell
- insulin resistance
- end stage renal disease
- pregnancy outcomes
- healthcare
- weight loss
- cardiovascular disease
- chronic kidney disease
- pregnant women
- weight gain
- postmenopausal women
- young adults
- adipose tissue
- systematic review
- ejection fraction
- multiple sclerosis
- randomized controlled trial
- physical activity
- preterm birth
- gene expression
- squamous cell carcinoma
- polycystic ovary syndrome
- chronic pain
- quality improvement
- bipolar disorder
- climate change
- gestational age
- high fat diet induced
- meta analyses
- genome wide
- preterm infants