Risk factors associated with mortality in neonatal intrahepatic cholestasis caused by citrin deficiency (NICCD) and clinical implications.
Kuerbanjiang AbuduxikuerRui ChenZhong-Lin WangKuerbanjiang AbuduxikuerPublished in: BMC pediatrics (2019)
Late referral, presence of infection, delayed treatment with LF/MCT formula, lower platelet count, lower levels of GGT, total cholesterol, blood citrulline, and higher level of blood ammonia and tyrosine, were associated with poor prognosis in NICCD.