Pathogenic role and diagnostic utility of interferon-α in histiocytic necrotizing lymphadenitis.
Shuya KanekoAsami ShimboHitoshi IrabuMaho HatanoKei TakasawaTakahiro KamiyaKeiji AkamineTakayuki TanakaToshinori MinatoMakoto OnoKoji YokoyamaAtsuko ArisakaTakahiro YasumiKazuyuki UenoShuhei FujitaYumi TanakaDaisuke HayashiHiroki NishikawaYuji FujitaYuki YuzaMasaaki MoriTomohiro MorioMasaki ShimizuPublished in: Clinical immunology (Orlando, Fla.) (2024)
IFN-α overproduction from pDCs may play a critical role in HNL pathogenesis. The serum IFN-α level may be a valuable biomarker for the diagnosis and monitoring of disease activity in patients with HNL.