Diagnosis of isolated hilar-/extrahepatic-type IgG-4-related sclerosing cholangitis can be increased by improved recognition of this condition-A Japanese multicenter analysis.
Kensuke KubotaEisuke IwasakiTakuya IshikawaMasaki KuwataniMamoru TakenakaTakuji IwashitaAtsuhiro MasudaTsukasa IkeuraAkira NakamuraAtsushi TanakaHiroyuki IsayamaYoshiki HirookaKenji HiranoShomei RyozawaTakeshi OguraToshio FujisawaYusuke KuritaKazuhiro KikutaNobuhiko HayashiAtsushi MasamuneIchiro YasudaPublished in: Journal of hepato-biliary-pancreatic sciences (2024)
Our validation of the 2020 criteria for the diagnosis of IgG4-SC could contribute to avoiding unnecessary resection in patients with isolated IgG4-SC, which can be classified into the hilar and extrahepatic types. The 2020 criteria can enhance the diagnosis rate of isolated IgG4-SC and uncover this tough-to-diagnose entity based on inclusion of the imaging findings and decrease the dependence on a steroid trial.