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Application and performance of disease activity indices proposed for patients with systemic sclerosis in an international cohort of patients with juvenile systemic sclerosis.

Jens KlotscheKathryn S TorokOzgur KasapcopurAmra AdrovicMaria Teresa TerreriAna Paula SakamotoMaria KatsicasFlavio SztajnbokEdoardo MarraniAlberto Sifuentes-GiraldoValda StanevichaJordi AntónBrian FeldmannMikhail KostikDana NemcovaMaria Jose SantosSimone AppenzellerTadej AvcinCristina BattagliottiLillemor BerntsonBlanca BicaJürgen BrunnerDespina EleftheriouLiora HarelGerd HorneffTilmann KallinichKirsten MindenSusan NielsenAnjali PatwardhanNicola HelmusIvan Foeldvari
Published in: Journal of scleroderma and related disorders (2023)
Overall, no disease activity score is superior to the other, and all three scores have limitations in the application in juvenile systemic sclerosis patients. Furthermore, research on the concept of disease activity and suitable scores to measure disease activity in patients with juvenile systemic sclerosis is necessary in future.
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