Application of tandem mass spectrometry in the screening and diagnosis of mucopolysaccharidoses.
Jing-Wen LiShao-Jia MaoYun-Qi ChaoChen-Xi HuYan-Jie QianYang-Li DaiKe HuangZheng ShenChao Chun ZouPublished in: Orphanet journal of rare diseases (2024)
Mucopolysaccharidoses (MPSs) are caused by a deficiency in the enzymes needed to degrade glycosaminoglycans (GAGs) in the lysosome. The storage of GAGs leads to the involvement of several systems and even to the death of the patient. In recent years, an increasing number of therapies have increased the treatment options available to patients. Early treatment is beneficial in improving the prognosis, but children with MPSs are often delayed in their diagnosis. Therefore, there is an urgent need to develop a method for early screening and diagnosis of the disease. Tandem mass spectrometry (MS/MS) is an analytical method that can detect multiple substrates or enzymes simultaneously. GAGs are reliable markers of MPSs. MS/MS can be used to screen children at an early stage of the disease, to improve prognosis by treating them before symptoms appear, to evaluate the effectiveness of treatment, and for metabolomic analysis or to find suitable biomarkers. In the future, MS/MS could be used to further identify suitable biomarkers for MPSs for early diagnosis and to detect efficacy.
Keyphrases
- tandem mass spectrometry
- ultra high performance liquid chromatography
- ms ms
- high performance liquid chromatography
- liquid chromatography
- simultaneous determination
- early stage
- gas chromatography
- liquid chromatography tandem mass spectrometry
- mass spectrometry
- solid phase extraction
- high resolution mass spectrometry
- young adults
- high resolution
- end stage renal disease
- systematic review
- randomized controlled trial
- newly diagnosed
- ejection fraction
- peritoneal dialysis
- radiation therapy
- replacement therapy
- prognostic factors
- chronic kidney disease
- squamous cell carcinoma
- case report
- patient reported outcomes
- living cells
- fluorescent probe