Elexacaftor/Tezacaftor/Ivacaftor in Patients with Cystic Fibrosis Homozygous for the F508del Mutation and Advanced Lung Disease: A 48-Week Observational Study.
Vincenzo CarnovalePaola IacotucciVito TerlizziCarmela ColangeloLorenza FerrilloAngela PepeMichela FrancalanciGiovanni TaccettiSerena BuonaurioAssunta CelardoLaura SalvadoriGiovanni MarsicovetereMichele D'AndriaNicola FerraraDonatello SalvatorePublished in: Journal of clinical medicine (2022)
genotype, ETI was safe and associated with clinical improvement.