Aggressive progressive pleuroparenchymal fibroelastosis developed long after allogenic hematopoietic stem cell transplantation.

Published in: Clinical case reports (2024)

The typical pleuroparenchymal fibroelastosis (PPFE) after hematopoietic stem cell transplantation (HSCT) is characterized by late-onset progressive pulmonary complication within 5 years. PPFE shows a poor prognosis without definitive standard care other than lung transplantation. Our case indicated an over 20 years late-onset and aggressively exacerbating PPFE.

Keyphrases

late onset
poor prognosis
multiple sclerosis
long non coding rna
early onset
acute myeloid leukemia
healthcare
palliative care
pulmonary hypertension
extracorporeal membrane oxygenation
quality improvement
radiation therapy
pain management
squamous cell carcinoma
chronic pain