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Prognostic factors of progressive fibrotic hypersensitivity pneumonitis: a large, retrospective, multicentre, observational cohort study.

Esteban Cano-JiménezAna Villar GómezEduardo Velez SegoviaMyriam AburtoJacobo Sellarés TorresJoel FrancesquiKarina Portillo CarrozAlan Jhunior Solis SolisOrlando Acosta FernándezAna Belén Llanos GonzálezJaume Bordas-MartinezEva Cabrera CesarEva Balcells VilarnauDiego CastilloAna Reyes PardessusCoral González FernándezMarta García MoyanoAmaia Urrutia GajateAndrés Blanco HortasMaría Molina-Molina
Published in: ERJ open research (2024)
The study identified several prognostic factors for progression and/or survival in fHP. The presence of fibroblastic foci at biopsy was a consistent predictor for increased mortality and the presence of lymphocytosis in BAL was inversely related to mortality.
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