Login / Signup

Transcriptomic signature of painful human neurofibromatosis type 2 schwannomas.

Phanidhar KukutlaSherif G AhmedDaniel M DuBreuilAhmed AbdelnabiMurat CetinbasGiulia FulciBerent AldikactiAnat Stemmer-RachamimovScott R PlotkinBrian WaingerRuslan I SadreyevGary J Brenner
Published in: Annals of clinical and translational neurology (2021)
Schwannomas are benign neoplasms that can cause gain- and loss-of-function neurological phenotypes, including severe, intractable pain. To investigate the molecular mechanisms underlying schwannoma-associated pain we compared the RNA sequencing profile of painful and non-painful schwannomas from NF2 patients. Distinct segregation of painful and non-painful tumors by gene expression patterns was observed. Differential expression analysis showed the upregulation of fibroblast growth factor 7 (FGF7) in painful schwannomas. Behavioral support for this finding was observed using a xenograft human NF2-schwannoma model in nude mice. In this model, over-expression of FGF7 in intra-sciatically implanted NF2 tumor cells generated pain behavior compared with controls.
Keyphrases