Reduction of spermine synthase enhances autophagy to suppress Tau accumulation.
Xianzun TaoJiaqi LiuZoraida Diaz-PerezJackson R FoleyAshley NwaforTracy Murray StewartRobert A CaseroRong Grace ZhaiPublished in: Cell death & disease (2024)
Precise polyamine metabolism regulation is vital for cells and organisms. Mutations in spermine synthase (SMS) cause Snyder-Robinson intellectual disability syndrome (SRS), characterized by significant spermidine accumulation and autophagy blockage in the nervous system. Emerging evidence connects polyamine metabolism with other autophagy-related diseases, such as Tauopathy, however, the functional intersection between polyamine metabolism and autophagy in the context of these diseases remains unclear. Here, we altered SMS expression level to investigate the regulation of autophagy by modulated polyamine metabolism in Tauopathy in Drosophila and human cellular models. Interestingly, while complete loss of Drosophila spermine synthase (dSms) impairs lysosomal function and blocks autophagic flux recapitulating SRS disease phenotype, partial loss of dSms enhanced autophagic flux, reduced Tau protein accumulation, and led to extended lifespan and improved climbing performance in Tauopathy flies. Measurement of polyamine levels detected a mild elevation of spermidine in flies with partial loss of dSms. Similarly, in human neuronal or glial cells, partial loss of SMS by siRNA-mediated knockdown upregulated autophagic flux and reduced Tau protein accumulation. Importantly, proteomics analysis of postmortem brain tissue from Alzheimer's disease (AD) patients showed a significant albeit modest elevation of SMS level. Taken together, our study uncovers a functional correlation between polyamine metabolism and autophagy in AD: SMS reduction upregulates autophagy, suppresses Tau accumulation, and ameliorates neurodegeneration and cell death. These findings provide a new potential therapeutic target for AD.
Keyphrases
- cell death
- cell cycle arrest
- endoplasmic reticulum stress
- induced apoptosis
- signaling pathway
- intellectual disability
- oxidative stress
- end stage renal disease
- endothelial cells
- poor prognosis
- newly diagnosed
- chronic kidney disease
- ejection fraction
- peritoneal dialysis
- risk assessment
- cognitive decline
- prognostic factors
- blood brain barrier
- drug delivery
- spinal cord
- human health
- cell proliferation
- drug induced
- cancer therapy
- patient reported
- white matter