Disappearing multiple visceral aneurysms in Vascular Ehlers-Danlos syndrome.
Federico Francisco PennettaCiro FerrerLuca TonidandelCarlo CoscarellaSimone VagnarelliRocco GiudicePublished in: Vascular (2023)
Both aneurysms were conservatively managed and the patient went through serial CT imaging. After 3 months, rapid regression of the vascular abnormalities led to complete disappearing of RRA and CHA aneurysms, confirmed at 24-month imaging follow-up. In the same time span, two pseudoaneurysms developed in other sites used for transarterial access, requiring two secondary interventions. The present case emphasizes the unpredictability of disease's evolution and arterial complications in vEDS. Conservative management of complex lesions such as visceral artery aneurysms, which in this case resulted to be the best strategy, avoided the risks associated with surgical intervention in such fragile tissues. The reported complications underline that operative indications should be carefully weighed in these patients.
Keyphrases
- high resolution
- end stage renal disease
- ejection fraction
- insulin resistance
- newly diagnosed
- randomized controlled trial
- risk factors
- case report
- computed tomography
- gene expression
- peritoneal dialysis
- prognostic factors
- magnetic resonance imaging
- physical activity
- patient reported outcomes
- mass spectrometry
- risk assessment
- fluorescence imaging
- adipose tissue
- skeletal muscle
- sensitive detection
- liver metastases