Expressing a Z-disk nebulin fragment in nebulin-deficient mouse muscle: effects on muscle structure and function.
Frank LiJustin KolbJulie CrudelePaola ToninoZaynab HouraniJohn E SmithJeffrey S ChamberlainHenk L GranzierPublished in: Skeletal muscle (2020)
This study reveals that nebulin fragments are well-received by nebulin-deficient mouse muscles and that limited functional benefits are achievable.
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