Congenital pulmonary airway malformation.
Wlamir Pestana UrsiniCesar Cilento PoncePublished in: Autopsy & case reports (2018)
Congenital pulmonary airway malformation (CPAM) is a developmental malformation of the lower respiratory tract. We report the case of a male newborn diagnosed with cystic lung disease during prenatal ultrasound. A cesarean section was performed at the 32nd gestational week because of premature rupture of the membranes, and soon after the delivery the newborn developed respiratory failure and died. The aim of this study is to report an autopsy case because of its rarity, and to briefly discuss the CPAM subtypes and differential diagnosis of cystic lung diseases of childhood.
Keyphrases
- respiratory tract
- respiratory failure
- pulmonary hypertension
- pregnant women
- extracorporeal membrane oxygenation
- magnetic resonance imaging
- weight gain
- mechanical ventilation
- randomized controlled trial
- clinical trial
- intensive care unit
- physical activity
- acute respiratory distress syndrome
- young adults
- childhood cancer
- weight loss