Clinical and neuroanatomical characterization of the semantic behavioral variant of frontotemporal dementia in a multicenter Italian cohort.
Alma GhirelliEdoardo Gioele SpinelliElisa CanuSilvia BasaiaVeronica CastelnovoGiordano CecchettiElisa SibillaTeuta DomiGiuseppe MagnaniFrancesca CasoPaola CaroppoSara PrioniCristina VillaGiacomina RossiLucio TremolizzoIldebrando AppollonioFederico VerdeNicola TicozziVincenzo SilaniMassimo FilippiFederica AgostaPublished in: Journal of neurology (2024)
We replicated the application of sbvFTD diagnostic guidelines in an independent Italian cohort, demonstrating that the presence of person-specific semantic knowledge loss and mental rigidity, along with preserved executive functions and a predominant right ATL atrophy with sparing of frontal lobes, should prompt a diagnosis of sbvFTD.