Rheology of right ventricular outflow tract obstruction: sub-pulmonary membrane developing months after primary intervention to treat pulmonary atresia with intact interventricular septum.
Baher Matta HannaWesam E El-MozySonia A El-SaiediPublished in: Cardiology in the young (2021)
Isolated sub-pulmonary membrane is a rare condition, the origin of which has been debatable. Transcatheter treatment of pulmonary valve atresia with intact interventricular septum by radiofrequency perforation and balloon dilatation to restore biventricular circulation is gaining more popularity, with improving results over time. We report in our experience of 79 cases in 10 years the development of a sub-pulmonary membrane in 4 cases: causing significant obstruction requiring surgical excision in one case that revealed a fibrous membrane on pathology; causing mild right ventricular outflow tract obstruction in another and not yet causing obstruction in 2. On cardiac MRI, the right ventricular outflow tract and the right ventricular outflow tract/pulmonary atresia angle showed no morphological abnormalities.
Keyphrases
- pulmonary hypertension
- randomized controlled trial
- magnetic resonance imaging
- high resolution
- aortic valve
- heart failure
- computed tomography
- single cell
- magnetic resonance
- contrast enhanced
- combination therapy
- aortic stenosis
- ultrasound guided
- transcatheter aortic valve replacement
- diffusion weighted imaging
- catheter ablation
- ejection fraction