Evaluating international Haemophilia Joint Health Score (HJHS) results combined with expert opinion: Options for a shorter HJHS.
Isolde A R KuijlaarsJanjaap van der NetBrian M FeldmanMagnus AspdahlMelanie BladenWypke de BoerCuesta-Barriuso RRuth Elise D MatlarySharon M FunkPamela HilliardJudy A JohnChristine L KemptonPiet de KleijnMarilyn J Manco-JohnsonPia PetriniPradeep Mathew PoonnooseJean St-LouisSylvia ThomasMerel A TimmerSonata Saulyte TrakymieneLeo van VlimmerenKathelijn FischerPublished in: Haemophilia : the official journal of the World Federation of Hemophilia (2020)
Analysis of 499 children and young adults with haemophilia showed that the HJHS is able to discriminate between children and adults and different treatment regimens. Reduction of the items 'duration swelling' and 'crepitus' resulted in the HJHSshort , which had the same discriminative ability. Additional steps are needed to achieve a substantially shorter HJHS assessment.