Radiologic pleuroparenchymal fibroelastosis-like lesion in connective tissue disease-related interstitial lung disease.
Yasunori EnomotoYutaro NakamuraThomas V ColbyTakeshi JohkohHiromitsu SumikawaKoji NishimotoKatsuhiro YoshimuraSayomi MatsushimaYoshiyuki OyamaHironao HozumiMasato KonoTomoyuki FujisawaNoriyuki EnomotoNaoki InuiToshihide IwashitaTakafumi SudaPublished in: PloS one (2017)
In patients with CTD-related ILD, radiologic PPFE-like lesion, which may present as not only PPFE but also apical cap and upper lobe subpleural fibrosis commonly due to UIP, was not uncommon and was associated with poor prognosis. Clinicians should be cautious with this radiologic finding, particularly when it is progressive.