Anesthetic management of multiple acyl-coenzyme A dehydrogenase deficiency in a series of surgeries under general anesthesia: a case report.
Ryoko Owaki-NakanoMidoriko HigashiKohei IwashitaKenji ShigematsuEmiko ToyamaKen YamauraPublished in: JA clinical reports (2021)
To avoid catabolism in patients with glutaric acidemia, appropriate glucose administration is important, depending on the surgical risk.