Progressive fibrosis in interstitial lung diseases - proposed definition and management.
Magdalena Maria Martusewicz-BorosWojciech Jerzy PiotrowskiPublished in: Advances in respiratory medicine (2022)
Interstitial lung diseases may have an unpredictably progressive course, which is manifested as progression of pulmonary fibrosis, causing an increasing impairment of lung function affecting a poor prognosis. The possibility of an effective antifibrotic treatment is a chance for patients to slow down the progression of the disease, perhaps even extend their life. For this reason, standardization of the definition as well as identification criteria for progressive fibrosis interstitial lung disease is a method for optimizing the management in this group of patients.
Keyphrases
- poor prognosis
- end stage renal disease
- lung function
- interstitial lung disease
- multiple sclerosis
- newly diagnosed
- ejection fraction
- chronic kidney disease
- pulmonary fibrosis
- systemic sclerosis
- prognostic factors
- peritoneal dialysis
- long non coding rna
- air pollution
- cystic fibrosis
- rheumatoid arthritis
- patient reported outcomes
- smoking cessation