Continuous use of glycomacropeptide in the nutritional management of patients with phenylketonuria: a clinical perspective.

Maria João PenaAlex PintoManuela Ferreira de AlmeidaCatarina de Sousa BarbosaPaula Cristina RamosSara RochaArlindo GuimasRosa RibeiroEsmeralda MartinsAnabela BandeiraCláudia Camila DiasAnita MacDonaldNuno BorgesJúlio César Rocha

Published in: Orphanet journal of rare diseases (2021)

Biochemical nutritional markers remained unchanged which is an encouraging finding in adults with PKU, many of whom are unable to maintain full adherence with nutritionally fortified protein substitutes. Longitudinal, prospective studies with larger sample sizes are necessary to fully understand the metabolic impact of using CGMP-AA in PKU.

Keyphrases

nitric oxide
cross sectional
protein protein
protein kinase
case control
amino acid
binding protein
type diabetes
metabolic syndrome
glycemic control