MATRIN3 deficiency triggers autoinflammation via cGAS-STING activation.
Zohirul IslamAhsan PolashMasataka SuzawaBryan ChimSkyler KuhnSabrina SultanaNicholas CutronaPatrick T SmithJuraj KabatSundar GanesanAmir ForoushaniMarkus HafnerStefan A MuljoPublished in: bioRxiv : the preprint server for biology (2024)
) in the absence of MATR3 unleashes R-loops and interferon-stimulated genes.