AA amyloidosis complicating cryopyrin-associated periodic syndrome: a study of 86 cases including 23 French patients and systematic review.

François RodriguesLaurence CuissetBérangère Cador-RousseauIrina GiurgeaBenedicte NevenDavid BuobPierre Quartier Dit MaireEric HachullaThierry LequerréGérard CamGuilaine BoursierValérie HervieuGilles GrateauSophie Georgin-Lavialle

Published in: Rheumatology (Oxford, England) (2022)

AA amyloidosis can occur in nearly all CAPS subtypes. IL-1 inhibitors are effective, underlining the necessity of an early diagnosis of CAPS in order to start this treatment as soon as possible among AA-CAPS patients.

Keyphrases

systematic review
end stage renal disease
ejection fraction
newly diagnosed
randomized controlled trial
patient reported outcomes
combination therapy