Fontan operation for tricuspid atresia with absent pulmonary valve: a case series.
Moyu HasegawaShigemitsu IwaiYosuke KugoPublished in: Cardiology in the young (2021)
Combined tricuspid atresia and absent pulmonary valve with dysplasia of the right ventricular myocardium is a very rare congenital heart anomaly with a poor prognosis. We present three cases of this rare disease that reached the Fontan operation without prior surgical intervention of the right ventricle or pulmonary artery; no right ventriclar dilation was detected. All patients had uneventful post-operative courses.
Keyphrases
- pulmonary artery
- pulmonary hypertension
- mitral valve
- poor prognosis
- aortic valve
- aortic stenosis
- ejection fraction
- coronary artery
- pulmonary arterial hypertension
- long non coding rna
- transcatheter aortic valve replacement
- end stage renal disease
- randomized controlled trial
- newly diagnosed
- left ventricular
- prognostic factors
- peritoneal dialysis