Elusive sources of variability of dystrophin rescue by exon skipping.
Maria Candida VilaMargaret Benny KlimekJames S NovakSree RayavarapuKitipong UaesoontrachoonJessica F BoehlerAlyson A FiorilloMarshall W HogarthAiping ZhangConner ShaughnessyHeather Gordish-DressmanUmar BurkiVolker StraubQi Long LuTerence A PartridgeKristy J BrownYetrib HathoutJohn van den AnkerEric P HoffmanKanneboyina NagarajuPublished in: Skeletal muscle (2015)
While we found some evidence of muscle group enhancement and successful rescue, our data also suggest that other yet-undefined factors may underlie the observed variability in the success of exon skipping. Our study highlights the challenges associated with quantifying dystrophin in clinical trials where a single small muscle biopsy is taken from a DMD patient.