Challenging Diagnosis of Anomalous Origin of the Right Coronary Artery from the Pulmonary Artery.
Hiyam MahmoudEliza Elena CintezăCristiana VoicuIrina MărgărintIulian RotaruAmelia AriaTammam YoussefAlin NicolescuPublished in: Diagnostics (Basel, Switzerland) (2022)
Anomalous origin of the right coronary artery (RCA) from the pulmonary artery, ARCAPA, is an extremely rare congenital heart disease. Only 200 cases were reported from 1885 to the present. Patients diagnosed with ARCAPA can be either asymptomatic or can experience symptoms, such as heart murmur, dyspnea, or angina, shortly after birth or around 40-60 years of life. Usually, those with isolated ARCAPA are diagnosed later in life compared to those who associate other structural cardiac defects. We report two cases of anomalous origin of the right coronary artery at the level of the pulmonary artery trunk (ARCAPA) that were diagnosed by invasive coronary angiography. Although asymptomatic, general recommendations suggest an early corrective intervention to prevent complications such as myocardial ischemia and cardiac dysfunction, which can lead to sudden cardiac death.
Keyphrases
- pulmonary artery
- coronary artery
- congenital heart disease
- left ventricular
- pulmonary hypertension
- end stage renal disease
- pulmonary arterial hypertension
- ejection fraction
- randomized controlled trial
- chronic kidney disease
- heart failure
- prognostic factors
- oxidative stress
- risk factors
- percutaneous coronary intervention
- physical activity
- atrial fibrillation
- patient reported outcomes
- advanced cancer
- pregnancy outcomes