Medullary thyroid cancer with ectopic Cushing's syndrome: A multicentre case series.
Viktoria Florentine KoehlerCarmina T FussChristina M BerrKarin Frank-RaueFriedhelm RaueEva HosterMatthias HepprichEmanuel ChristThomas PuslMartin ReinckeChristine SpitzwegMatthias Kroissnull nullPublished in: Clinical endocrinology (2021)
This study shows that ECS occurs in advanced stage MTC and is associated with a poor prognosis. Adrenostatic treatment and BADX were effective systemic treatment options in patients with MTC and ECS to control their hypercortisolism. MKI treatment achieved complete remission of hypercortisolism and sustained tumour control in one treated case.